Case #19 – AZOOR or RP?

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Suggested Readings Witkin AJ, Ko TH, Fujimoto JG, et al. Ultra-high Resolution Optical Coherence Tomography Assessment of Photoreceptors In Retinitis Pigmentosa and Related Diseases. Am J Ophthalmol 2006; 142: 945-952.Murakami T, Akimoto M, et al. Association Between Abnormal Autofluorescence and Photoreceptor Disorganization in Retinitis Pigmentosa. Am J Ophthalmol 2008; 145: 687-694.Farrell DF. Unilateral retinitis pigmentosa

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References Gass JDM. Acute Zonal Occult Outer Retinopathy. Journal of Clinical Neuro-ophthalmology 1993; 13(2): 79-97. Pagon RA, Daiger SP. Retinitis Pigmentosa Overview. Gene Reviews-NCBI Bookshelf 2005. Zacks DN, Johnson MW, Arbor A. Transretinal Pigment Migration: An Optical Coherence Tomographic Study. Arch Ophthalmol 2004; 122: 406-408. Campochiaro PA, Jerdan JA, et al. Vitreous Aspirates from Patients

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Jerome Sherman, OD, FAAO Jerome Sherman, O.D., is perhaps optometry's most prolific writer, publishing over 650 clinical articles, research manuscripts, book chapters and two CDs. He is senior author of three books that were published in 2007, and has delivered over three thousand lectures both nationally and internationally. He has served as a contributing

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Comments and Conclusions This case represents a rare opportunity to evaluate a patient who was one of the original 13 described by Dr. Gass in his 1993 intriguing and ground breaking article that described AZOOR for the first time.1 If our patient was seen without 2 decades of detailed records, the probable diagnosis at

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Composite of Central and Peripheral Fields OS Shown is the left eye composite central and peripheral fields. No visual field was measurable in the right eye.

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Central and Peripheral Visual Fields OS (10-23-9) On recent visual fields (10-23-09) both central and peripheral visual fields are markedly abnormal in the left eye. No field was measurable in the right eye with Hand Motion VA.

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Central and Peripheral Visual Fields OD (8-51-88) Much of the central field defect in the right eye as revealed with the 24-2 extends to the periphery as demonstrated with the 60-4 in the right eye above.

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Central Visual Fields (8-51-88) Visual fields with the 24-2 program back in 1988 reveal a dense superior arcuate scotoma OD and an enlarged blind spot OS. There was no corresponding retinal abnormality visible with ophthalmoscopy.

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