Case #29 – Proliferative Sickle Cell Retinopathy (PSR)

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Diagnostic Challenge The traditional FA camera can allow only a 50- degree field of view of posterior pole imaging. or 75-degree field of view with composite images15. And we still do not see the areas of peripheral vasculopathy previously demonstrated in Case 1. There have been reports on using

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In contrast to a "normal" optos® FA, note the dramatic avascularity in all four quadrants of the mid and far periphery. The patient is being treated with Anti-VEGF injections and PRP. Case 7: Patient vs. "Normal" Optomap® Fluorescein Angiography Fundus Images of Right Eye

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Case 6: Optomap® Fluorescein Angiography Image of Left Eye Patient has lupus, no visual symptoms, 20/20 VA in each eye and a mild far peripheral retinopathy OU which is most marked temporally in both eyes.

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Case 6: Optomap® Fluorescein Angiography Image of Right Eye Patient has lupus, no visual symptoms, 20/20 VA in each eye and a mild far peripheral OU which is most marked temporally in both eyes.

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Case 3: Optosmap® Fluorescein Angiography Image of Right Eye A 62-year-old female diagnosed with MTHFR (methione tetrahydrofolate reductase) recessive hypercoagulopathy VA 20/25 and 20/20. (Images courtesy of Juliana Boneta, OD and Karl Waite, MD.)

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The large lesion in the left eye had substantial leakage, zones of avascularity, and aneurysmal dilatations. The patient was diagnosed with Coats-like Peripheral Retinopathy. Recent genetic testing revealed the patient has Facioscapulohumeral Muscular Dystrophy (FSHD) which is known to be associated with Coats-like retinopathy. For the complete Retina Revealed Issue of this case

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Case 3: Optos® Fluorescein Angiography Sickle Cell Retinopathy A third exemplary case of PSR utilizing an optos® fluorescein angiography. Note the two large characteristic "sea fans" and zones of avascularity in the temporal periphery as previously demonstrated in Cases 1 and 2.

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