Case #13 – Fundus Albipunctatus with Cone Dystrophy

Summary Cirrus™ HD-OCT OS The Summary Cirrus™ findings in the left eye are quite similar to the findings in the right eye on the previous page.

Summary Cirrus™ HD-OCT OD The macula region is very attenuated in thickness as revealed by comparison to the normative database. All zones are flagged in red and hence only 1% of normal eyes have values as thin as our patient.

Using the vessel above the lesion as a landmark, the macula lesion clearly has increased in size over the 12 year period. In Fundus Albi, the dots generally fade slowly over decades.

OS July 1997  Standard fundus photography of the left posterior pole.

OS June 2009   Standard fundus photography of the left posterior pole.

Topcon 3D OCT OS June 2009 Each white vertical line corresponds to the green vertical cross-hatch. Between the vertical lines, the RPE and PIL are visible. Outside the vertical lines, only Bruch's membrane is visible.

Cirrus­™ HD-OCT OS Few if any dots are visualized in the macula region. Grey scale OCT often appear to reveal subtle detail better than the color OCT images.

Cirrus™ HD-OCT OD OCT sections of the atrophic central lesion reveal a very thin macula and a well visualized Bruch's membrane. When the RPE is lost, Bruch's membrane which is under the RPE is unmasked and becomes prominent.

Topcon 3D OCT OD June 2009 In these horizontal sections as well, the dots appear to straddle the somewhat disorganized PIL.

Topcon 3D OCT OS June 2009 Horizontal SD OCT under magnified and increased contrast conditions. The dots appear to straddle the PIL which is somewhat disorganized.