Case #15 – Bietti with Outer Retinal Tubulations

Optomap® color fundus image of right eye The choroidal vessels are quite prominent ("choroidal sclerosis") around the disc. Pigment clumping as well as subtle tiny white dots are widespread.

History/Chief Complaints 43 yo male with a history of reduced day vision over the past year, right eye greater than left, and progressive loss of night vision for over a decade OU. Reports that his older sister has a similar vision disorder. General health history reported as unremarkable but his last exam was at least

Crystalline Retinopathies The Optos® fly through is particularly helpful for patient education in demonstrating the extent and location of retinal abnormalities. Optos optomap® color fundus of the left eye.

Glistening crystals in the retina can be due to myriad etiologies ranging from drug toxicity to a genetic retinal degeneration. This Week's Case is about a patient with both corneal crystals and retinal crystals, suggestive of Bietti corneoretinal degeneration. SD OCT not only confirms the dramatic loss of photoreceptors in this disorder but leads