Case #38 – Leber’s Hereditary Optic Neuropathy

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Case 1: maia™ Sensitivity Map OS In the left eye, most of the tested points have a normal threshold depicted in green with a few borderline sensitivity values depicted in yellow.

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Case 1: maia™ Sensitivity Map & Topcon 3D OCT Color Fundus Image OD A comparison of the maia™ field with the fundus image of the optic disc and peripapillary RNFL.

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Case 1: maia™ Sensitivity Map OD This maia™ pattern is equivalent to the standard 10-2 Humphrey Zeiss in which the stimuli are all 2 degrees apart. In contrast to the previous visual field which subtended the central 10 degrees, here the total field is 20 degrees.

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Leber’s Hereditary Optic Neuropathy – Page 9 of 56

Case 1: maia™ Sensitivity Map & Threshold Histogram OD The inner ring of stimuli is 1 degree from the central fixation point and the remaining 2 rings are each 2 degrees apart. Sensitivity values depicted in green are normal, those in yellow are borderline and those in red are quite reduced.

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Evaluates Macula Threshold, Fixation Stability & Change over time • Any maculopathy - AMD, Drug toxicity, Amblyopia or Unexplained vision loss • Plots progression of macular threshold and fixation stability • Demonstrates the effect of external treatment regimens to macular threshold & fixation stability

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maia™ (Macular Integrity Assessment) uses a near infrared scanning laser ophthalmoscope to provide high-resolution retinal images. It also incorporates an automated eye tracker to ensure point-to-point correspondence and consistency of examination as well as automated threshold perimetry to perform fundus perimetry. More traditionally this is called microperimetry and provides a functional evaluation of

Leber’s Hereditary Optic Neuropathy – Page 7 of 562021-05-05T21:04:44+00:00