Case #54 – AF in Myriad Retinal Degenerations- Part 1

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Case 5: Optomap® Color Fundus and AF Comparison OD and OS KEY: Color Optomap Auto Fluorescence Genetics in this and other cases presented herein have been initiated. ERGs are also planned. At the present time, the most likely diagnosis is a cone rod degeneration. Attempts to obtain uwf AF in young family

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Case 5: Optomap® plus with Resmax™ AF Image OD The AF image reveals hypo-AF in the posterior pole surrounded by an annulus of hyper-AF. The less dramatic abnormality inferior temporal to the disc is not typical of Central Areolar Choroidal Dystrophy (CACD). Symptoms of night vision difficulty are also not typical of CACD.

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Case 5: Optomap® plus with Resmax™ Color Image OD Case 5: A 40 yr HF presented for evaluation of possible CACD vs Code-Rod Degeneration. Patient reported difficulty with night vision more so than day vision since childhood. She did not report any color vision problems. Pigment hypertrophy and atrophy was noted in the macula of

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Case 4: Optomap® Color Fundus and AF Comparison OD and OS KEY: Color Optomap Auto Fluorescence Note the symmetry ( as also demonstrated in the previous cases) between the right and left eye. Such bilateral symmetry is quite typical of inherited retinal degenerations. The pattern of central degeneration in this case is often

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Case 4: Optomap® plus with Resmax™ AF Image OD The AF images reveals relative hypo-AF centrally in an oval pattern. The ring of hyper-AF surrounding the hypo-AF oval suggests that the condition is progressing toward the mid-periphery.

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Case 4: Optomap® plus with Resmax™ Color Image OD Case 4: 54 yo HF for follow up of probable Cone-Rod Dystrophy. The patient reports progressive loss of vision in both eyes with onset 8 years ago. The fundus abnormalities are subtle and include attenuated arterioles. ERGs showed a reduction in cone function greater than

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